Neurofibroma (within NF)

Author: Faculty Reviewer:

Publish date: Posted on
Last updated: May 25, 2022

Keywords #

neurofibroma
neurofibromatosis

Diagnosis #

Neurofibromas are well circumscribed, benign growths composed of neuromesenchymal tissue and residual nerve fibers.[1] They are common growths that can be seen as solitary nodules or in syndromes such as neurofibromatosis. Neurofibromas are usually soft or rubbery, skin-colored nodules that can range from a few millimeters up to 2 cm. Most neurofibromas can be treated by simple excision or shave removal, if desired.

Key Concepts #
  • Solitary neurofibromas are benign growths common in adults.
  • Many neurofibromas can be a sign of systemic disease such as neurofibromatosis, as can larger, “plexiform” neurofibromas.
  • Simple neurofibromas can be treated by simple excision or shave removal, but they generally require no treatment because they are benign growths.
Epidemiology #

Solitary neurofibromas are commonly found in adults in both men and women. [2]

Clinical Features #
  • Solitary, skin-colored, soft or rubbery papulonodules
  • Usually between a few millimeters and 2 cm
  • The “buttonhole” sign is commonly seen –meaning the tumor is easily invaginated
Differential Diagnoses #
Diagnostic Workup #

Neurofibromas are a clinical diagnosis. No diagnostic workup is necessary. [4] If a patient has more than one neurofibroma and other signs of neurofibromatosis, a work-up for this entity is warranted.

Treatment #

Neurofibromas can be removed by simple excision.

References #
  1. Bolognia, Jean, et al.Dermatology.[ElectronicResource]. Fourth edition., Elsevier, 2018.EBSCOhost,
  2. Kang, Sewon, et al.Fitzpatrick’sDermatology.[ElectronicResource]. 9th ed., McGraw-Hill Education LLC., 2019.EBSCOhost,
  3. Bolognia, Jean.DermatologyEssentials.[ElectronicResource]. Saunders, 2014.EBSCOhost,
  4. Soutor, Carol, and Maria K. Hordinsky.ClinicalDermatology.[ElectronicResource]. 1st ed., McGraw-Hill Education, 2013.EBSCOhost